EnvisionRheumat
EnvisionRheumat

@ERheumat

7 Tweets 50 reads Jun 04, 2022
#EULAR2022
Contrasts in pathomechanisms and treatment targets between adult and paediatric inflammatory myositis
πŸ‘β€πŸ—¨ Awesome class on IIM pathogenesis
πŸ‘β€πŸ—¨The MSA and Phenotype Slide is πŸ‘ŒπŸ»πŸ‘ŒπŸ»
#EULAR2022
Contrasts in pathomechanisms and treatment targets between adult and paediatric inflammatory myositis
πŸ‘β€πŸ—¨Summary of Mechanisms
πŸ‘β€πŸ—¨DM/JDMπŸ‘‰πŸ» CD4 and TH17 mediated
πŸ‘β€πŸ—¨ Both Inflammatory and non inflammatory factors contribute
#EULAR2022
πŸ‘β€πŸ—¨ Type I,II IFN sig
πŸ‘‰πŸ» DM/JDM>>ASS/PM>IBM>IMNM
πŸ‘‰πŸ» Mi2/TIF/MDA5>>Jo1>>SRP/HMCGR
πŸ‘β€πŸ—¨β¬†οΈINF levels πŸ‘‰πŸ»β¬†οΈ disease activity
πŸ‘β€πŸ—¨pDC and mDC mediated
πŸ‘β€πŸ—¨Mediate Muscle atrophy(perifasicular) and Capillary loss
#EULAR2022
Contrasts in pathomechanisms and treatment targets between adult and paediatric inflammatory myositis
πŸ‘β€πŸ—¨NETs & LDG⬆️ in Blood, Muscle, Lung & Skin
πŸ‘β€πŸ—¨MDA5 ⬆️NETs>>MJ,TIF,Jo1
#EULAR2022
πŸ‘β€πŸ—¨ Vasculopathy JDM>>>DM
πŸ‘β€πŸ—¨ Muscle damage in IIM us Multifactorial
πŸ‘β€πŸ—¨ DM πŸ‘‰πŸ» ⬆️INF, TNF, NF-KB
πŸ‘β€πŸ—¨IMNMπŸ‘‰πŸ» ⬆️APR and ⬇️ Lymphocyte response
πŸ‘β€πŸ—¨ASSπŸ‘‰πŸ» ⬆️APR, RNA binding ⬇️Muscle func, ubiquitination
#EULAR2022
πŸ‘β€πŸ—¨ Calcinosis JDM>>DM
πŸ‘β€πŸ—¨ CD3+ T Cells and Macrophages have a role
πŸ‘β€πŸ—¨ NETs engulf Ca crystals and Ca crystals cause NETOSIS
πŸ‘β€πŸ—¨Mitochondrial calcification
πŸ‘β€πŸ—¨ ⬆️ SIBLING protein expression
#EULAR2022
Contrasts in pathomechanisms and treatment targets between adult and paediatric inflammatory myositis
Summary Slides

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